n SA Journal of Radiology - Imaging features of a rare case of scapuloiliac dysostosis (Kosenow syndrome) in an ambulatory child : case report
|Article Title||Imaging features of a rare case of scapuloiliac dysostosis (Kosenow syndrome) in an ambulatory child : case report|
|Journal||SA Journal of Radiology|
|Author||John Joseph, Harish Narayanan, Jacob Varghese, Harish Babu and A. Praveen|
|Publication Date||Mar 2011|
|Pages||6 - 7|
|Keyword(s)||Trivandrum Medical College|
Scapuloiliac dysostosis, also known as pelvis-shoulder dysplasia and Kosenow syndrome, is a rare skeletal dysplasia described first by Kosenow et al. in 1970. The main components of the syndrome are varying degrees of bilateral iliac and scapular hypoplasia. Various other skeletal abnormalities including exaggerated lumbar lordosis, and clavicular, vertebral, rib and long bone anomalies and extra-skeletal abnormalities, most commonly those of eye and ear, have also been reported. We report the plain radiography, CT and MRI findings of an interesting case of the syndrome.
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