n SA Journal of Radiology - MRI imaging of vein of Galen malformations at Steve Biko Academic Hospital : a mini case series : pictorial essay
|Article Title||MRI imaging of vein of Galen malformations at Steve Biko Academic Hospital : a mini case series : pictorial essay|
|Journal||SA Journal of Radiology|
|Author||Liesel Davel, Janet Smal and Z.I. Lockhat|
|Publication Date||Jun 2011|
|Pages||53 - 55|
|Keyword(s)||Steve Biko Academic Hospital, Pretoria|
Vein of Galen aneurysmal malformation (VOGM) is an arterio-venous fistula involving aneurysmal dilatation of the median prosencephalic vein of Markowski. Dilated arteries drain into a large midline venous pouch in the region of the quadrigeminal cistern. It is a rare condition and is demonstrated in less than 1% of cerebral vascular malformations at any age and up to 30% of paediatric vascular malformations. Associated clinical findings may include cardiomegaly, widened mediastinum, pulmonary oedema and cyanosis. Heart failure and cyanosis in infants almost always results from congenital heart disease, but systemic arterio-venous malformations are a rare cause for such a presentation and the diagnosis is often missed or delayed. The following is a discussion and presentation of MRI images of 4 patients with this rare condition who presented at Steve Biko Academic Hospital within a 2-year period.
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